Bilateral Renal Angiomyolipomas Giants

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Authors

  • Marta Molina Anguita Resident Medical Intern (MIR), Department of Familiar and Community Medicine, General Hospital, Ciudad Real, Spain
  • Luis Calahorra Fernández Director, Service of Urology, General Hospital, Ciudad Real, Spain

DOI:

https://doi.org/10.17140/UAOJ-1-104

Keywords:

Renal angiomyolipoma, neurofibromatosis, Von Reck linghausen disease (VRD), Tuberous Sclerosis (TS), mesenchymal neoplasm, dysmorphic vessels

Abstract

Renal angiomyolipoma is a rare benign mesenchymal neoplasm and is characterized by the presence of thin dysmorphic vessels, smooth muscle and adipose tissue. The incidence of renal angiomyolipoma is 0.1-0.3% and it can be presented as an isolated pathology or be associated with other entities, such as Tuberous Sclerosis (TS) or Bourneville’s disease, and Von Reck linghausen disease (VRD) or neurofibromatosis. We report a case of a female patient aged 22 with kidney angiolipomas giant associated with tuberous sclerosis, syndrome characterized by the formation of hamartomas and tumors in different organs of the body.

References

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Bestard Vallejo JE, Trilla Herrera E, Celma Domenech A, Pé-rez Lafuente M, de Torres Ramírez I, Morote Robles J. Servi-cio de Urología, Angio-Radiología y Anatomía Patológica del Hospital General Universitario Valld’Hebron. UAB. Barcelona. Angiomiolipomas renales: Presentación, tratamiento y resultado de 20 casos [In Spanish]. Actas Urol Esp. 2008; 32(3): 307-315. doi: 10.1016/S0210-4806(08)73835-X

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Published

2016-09-12

How to Cite

Marta Molina Anguita, & Luis Calahorra Fernández. (2016). Bilateral Renal Angiomyolipomas Giants. Urology and Andrology , 1(1), 15–17. https://doi.org/10.17140/UAOJ-1-104