Bilateral Renal Angiomyolipomas Giants

Abstract

Renal angiomyolipoma is a rare benign mesenchymal neoplasm and is characterized by the presence of thin dysmorphic vessels, smooth muscle and adipose tissue. The incidence of renal angiomyolipoma is 0.1-0.3% and it can be presented as an isolated pathology or be associated with other entities, such as Tuberous Sclerosis (TS) or Bourneville’s disease, and Von Reck linghausen disease (VRD) or neurofibromatosis. We report a case of a female patient aged 22 with kidney angiolipomas giant associated with tuberous sclerosis, syndrome characterized by the formation of hamartomas and tumors in different organs of the body.