Rhabdomyosarcoma (RMS) of the Renal Pelvis in a Child: A Case Report

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Authors

  • Vincenzo Domenichelli Pediatric Surgery Unit, Infermi Hospital, AUSL Romagna, Rimini, Italy
  • Simona Straziuso Pediatric Surgery Unit, Infermi Hospital, AUSL Romagna, Rimini, Italy
  • Francesco Italiano Pediatric Surgery Unit, Infermi Hospital, AUSL Romagna, Rimini, Italy
  • Gabriella Pelusi Pediatric Surgery Unit, Infermi Hospital, AUSL Romagna, Rimini, Italy
  • Silvana Federici Pediatric Surgery Unit, Infermi Hospital, AUSL Romagna, Rimini, Italy

DOI:

https://doi.org/10.17140/UAOJ-1-110

Keywords:

Rhabdomyosarcoma (RMS), Renal mass, Uro-MRI, Kidney biopsy

Abstract

Rhabdomyosarcomas (RMS) of the kidney is extremely rare. We are reporting one case of embrional rhabdomyosarcoma localized in a child renal pelvis, focusing on the rarity of the site and role of imaging. An 8-years-old boy was admitted to the hospital with abdominal pain and hematuria. Ultrasonography revealed a right ureteropyelectasy including an echogenic image that extended from the renal pelvis towards inferior basin with no hypervascularization, simulating a clot. The urography-magnetic resonance imaging (Uro-MRI) showed two different components of the lesion: the first one simulating a clot; the second one detected in the papillary region and extended to the inferior calices having tumor-like features. A percutaneous ultrasound-guided renal biopsy revealed a botryoid embryonal rhabdomyosarcoma. The RMS is a complex childhood malignancy. This complexity is reflected in the radiological assessment that remains highly challenging and in the absense of treatment guidelines for unusual sites.

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Published

2017-07-04

How to Cite

Vincenzo Domenichelli, Simona Straziuso, Francesco Italiano, Gabriella Pelusi, & Silvana Federici. (2017). Rhabdomyosarcoma (RMS) of the Renal Pelvis in a Child: A Case Report. Urology and Andrology , 1(2), 35–38. https://doi.org/10.17140/UAOJ-1-110

Issue

Vol. 1 No. 2 (2017): Volume 1 Issue 2 2017

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Articles

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