Anesthetic Considerations in a Case of Fahr and Primrose Syndrome

Authors

  • Bhavna Gupta DA, DNB Department of Anesthesia and ICU, Lok Nayak Hospital, New Delhi, India
  • Lalit Gupta DA, DNB Department of Anesthesia and ICU, Lok Nayak Hospital, New Delhi, India

DOI:

https://doi.org/10.17140/RPAOJ-3-116

Keywords:

Fahr syndrome, Primrose syndrome, Anesthesia, Calcium

Abstract

In this review article, brief description, concerns, anesthetic management and perioperative care patients with Fahr syndrome and Primrose syndrome has been made. There is a paucity of literature with respect to management of such cases. There are limited case reports reported in the literature. The literature search has been made by using Google scholar, PubMed, Medline, Medscape and other search-related search engines with the following keywords.

References

Morgante L, Trimarchi F, Benvenga S. Fahr’s disease. Lan-cet. 2002; 359: 759. doi: 10.1016/S0140-6736(02)07878-9 Submit your article to this journal | https://openventio.org/submit-manuscript/

Primrose DA. A slowly progressive degenerative condition char-acterized by mental deficiency, wasting of limb musculature and bone abnormalities, including ossification of the pinnae. J Ment Defic Res. 1982; 26: 101-106. doi: 10.1111/j.1365-2788.1982. tb00133.x

Lindor NM, Hoffman AD, Primrose DA. A neuropsychiatric disorder associated with dense calcification of the external ears and distal muscle wasting: ‘Primrose syndrome’”. Clin Dysmor-phol. 1996; 5: 27-34.

Belenli C, Arpaci AH. Anesthesiological approach to a case with FAHR syndrome. J Res Med Sci. 2014; 19: 286.

Aguilera IM, Vaughan RS. Calcium and the anaesthesist. Anaes-thesia. 2000; 55: 779-790. doi: 10.1046/j.1365-2044.2000.01540.x

Okçelik S, Tasdemir S, Öztürk E, Soydan H. Subinguinal Vari-cocelectomy under spinal anesthesia in a Fahr’s syndrome pa-tient with non-obstructıve azoospermia. Andrology. 5: 163. doi: 10.4172/2167-0250.1000163

Wappler F. Anesthesia for patients with history of malignant hyperthermia. Curr Opin Anaesthesiol. 2010; 23(3): 417-422. doi: 10.1097/ACO.0b013e328337ffe0

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Published

2018-02-28

How to Cite

Bhavna Gupta, & Lalit Gupta. (2018). Anesthetic Considerations in a Case of Fahr and Primrose Syndrome. Research and Practice in Anesthesiology, 3(1), 1–6. https://doi.org/10.17140/RPAOJ-3-116